🏠︎ » 2023 » Volume 81 - Number 4 » Atypical presentation of anti-NXP-2 positive juvenile dermatomyositis
Andreia Coimbra-Sousa 1, Renata Miossi 1, Fernando H. C. de Souza 1, Samuel Katsuyuki-Shinjo 1
1 Division of Rheumatology, Faculdade de Medicina FMUSP, Universidade de São Paulo, São Paulo, Brazil
Andreia Coimbra-Sousa, Renata Miossi, Fernando H. C. de Souza, Samuel Katsuyuki-Shinjo
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*Correspondence: Andreia Coimbra-Sousa, Email not available
Dear Editor, The anti-NXP-2 is one of a myositis-specific autoantibody considered a marker of dermatomyositis (DM)1,2. In addition, there is a strong relationship between NXP-2 autoantibodies and calcinosis, particularly in juvenile DM2.